Authors
Chris Miles, Gherardo Finocchiaro, Joseph Westaby, Joyee Basu, Gemma Parry-Williams, Bode Ensam, Stathis Papatheodorou, Hamish MacLachlan, Casey Paterson, Aneil Malhotra, Michael Papadakis, Sanjay Sharma, Elijah Behr, Mary Sheppard
Publication date
2018/6/1
Source
Heart
Volume
104
Issue
Suppl 6
Pages
A61-A62
Publisher
BMJ Publishing Group Ltd and British Cardiovascular Society
Description
Background
Arrhythmogenic cardiomyopathy (ACM) is an inherited heart muscle disorder characterised by fibrofatty replacement of the ventricular myocardium. It is a leading cause of sudden cardiac death (SCD) in young athletes, where morphological appearances of the right ventricle may overlap with physiological adaptation to regular intense exercise.
Purpose
Evaluation of sport classification, clinical characteristics, and pathological findings in a retrospective young SCD athletic population.
Methods
Between 1994–2017, 5205 consecutive cases of SCD were referred to our national cardiac pathology centre. Hearts were examined macroscopically and microscopically by an expert cardiac pathologist. 216 cases were diagnosed with ACM, of which 98 were aged 1435.
Information pertaining to circumstances of death, sporting activity, and symptoms were provided by coroners’ officers and family members …
Total citations
20201
Scholar articles
C Miles, G Finocchiaro, J Westaby, J Basu… - 2018