Authors
Aryeh Fischer, Katerina M Antoniou, Kevin K Brown, Jacques Cadranel, Tamera J Corte, Roland M Du Bois, Joyce S Lee, Kevin O Leslie, David A Lynch, Eric L Matteson, Marta Mosca, Imre Noth, Luca Richeldi, Mary E Strek, Jeffrey J Swigris, Athol U Wells, Sterling G West, Harold R Collard, Vincent Cottin
Publication date
2015/10/1
Journal
European Respiratory Journal
Volume
46
Issue
4
Pages
976-987
Publisher
European Respiratory Society
Description
Many patients with an idiopathic interstitial pneumonia (IIP) have clinical features that suggest an underlying autoimmune process but do not meet established criteria for a connective tissue disease (CTD). Researchers have proposed differing criteria and terms to describe these patients, and lack of consensus over nomenclature and classification limits the ability to conduct prospective studies of a uniform cohort.
The “European Respiratory Society/American Thoracic Society Task Force on Undifferentiated Forms of Connective Tissue Disease-associated Interstitial Lung Disease” was formed to create consensus regarding the nomenclature and classification criteria for patients with IIP and features of autoimmunity.
The task force proposes the term “interstitial pneumonia with autoimmune features” (IPAF) and offers classification criteria organised around the presence of a combination of features from three domains …
Scholar articles
A Fischer, KM Antoniou, KK Brown, J Cadranel… - European Respiratory Journal, 2015