Authors
Siddhartha G Kapnadak, Emily Dimango, Denis Hadjiliadis, Sarah E Hempstead, Erin Tallarico, Joseph M Pilewski, Albert Faro, James Albright, Christian Benden, Shaina Blair, Elisabeth P Dellon, Daniel Gochenour, Peter Michelson, Baharak Moshiree, Isabel Neuringer, Carl Riedy, Teresa Schindler, Lianne G Singer, Dave Young, Lauren Vignola, Joan Zukosky, Richard H Simon
Publication date
2020/5/1
Journal
Journal of Cystic Fibrosis
Volume
19
Issue
3
Pages
344-354
Publisher
Elsevier
Description
Background
Advanced cystic fibrosis lung disease (ACFLD) is common, is associated with reduced quality of life, and remains the most frequent cause of death in individuals with cystic fibrosis (CF). These consensus guidelines provide recommendations to the CF community on management of both common and unique issues that arise when individuals reach a state of ACFLD.
Methods
The CF Foundation assembled a multidisciplinary expert panel consisting of three workgroups: Pulmonary management; Management of comorbid conditions; Symptom management and psychosocial issues. Topics were excluded if the management considerations did not differ in ACFLD from in the overall CF population or if already addressed in other published guidelines. Recommendations were based on a systematic literature review combined with expert opinion when appropriate.
Results
The committee formulated twenty …
Scholar articles
SG Kapnadak, E Dimango, D Hadjiliadis… - Journal of Cystic Fibrosis, 2020