Authors
Melissa J Armstrong, Irene Litvan, Anthony E Lang, Thomas H Bak, Kailash P Bhatia, Barbara Borroni, Adam L Boxer, Dennis W Dickson, Murray Grossman, Mark Hallett, Keith A Josephs, Andrew Kertesz, Suzee E Lee, Bruce L Miller, Stephen G Reich, David E Riley, Eduardo Tolosa, Alexander I Tröster, Marie Vidailhet, William J Weiner
Publication date
2013/1/29
Source
Neurology
Volume
80
Issue
5
Pages
496-503
Publisher
Lippincott Williams & Wilkins
Description
Current criteria for the clinical diagnosis of pathologically confirmed corticobasal degeneration (CBD) no longer reflect the expanding understanding of this disease and its clinicopathologic correlations. An international consortium of behavioral neurology, neuropsychology, and movement disorders specialists developed new criteria based on consensus and a systematic literature review. Clinical diagnoses (early or late) were identified for 267 nonoverlapping pathologically confirmed CBD cases from published reports and brain banks. Combined with consensus, 4 CBD phenotypes emerged: corticobasal syndrome (CBS), frontal behavioral-spatial syndrome (FBS), nonfluent/agrammatic variant of primary progressive aphasia (naPPA), and progressive supranuclear palsy syndrome (PSPS). Clinical features of CBD cases were extracted from descriptions of 209 brain bank and published patients, providing a …
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MJ Armstrong, I Litvan, AE Lang, TH Bak, KP Bhatia… - Neurology, 2013